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Phenylketonuria treatment, dietary therapy, nutritional advice

Homepage Articles Phenylketonuria treatment, dietary therapy, nutritional advice

Phenylketonuria treatment, dietary therapy, nutritional advice

Some foods may be on the daily menu, but there are also foods that should be completely eliminated from the menu. These should be used throughout life to prevent the negative consequences of the disease.

Table of Contents

1. Phenylketonuria basic information

Concentration problems, learning difficulties and excessive motor activity are just some of the symptoms of high levels of phenylalanine in the blood. The introduction of appropriate treatment can prevent these negative changes (D. The use of a diet with a limited supply of phenylalanine is the basis of therapy. It is recommended to modify the life of the baby during pregnancy (E. Rodington 2020).

2. The following is a summary of the results of the evaluation:

The low-phenylalanine diet should be used throughout life, but its role is particularly highlighted as early as infancy. Two options are recommended. The second option is to feed the mother's food, but it must be prepared beforehand. In the case of breastfeeding, the food should be withdrawn first and measured accordingly. The tolerance of phenyloalanine in infants is slightly higher than that in adults, but this is associated with intense growth. For older children, the tolerance is 1020 mg/kg of body weight per day, whereas in adults the levels of amino acids per 510 kg of body mass per day depend on the body weight of the diet (e.g. the effect of dietary changes in the use of phenylphenyls does not affect the health of infants, and in most cases, it is not). In order to reduce the amount of protein in the diet of newborn babies, it should be limited to 100 mg per day. For example, in order to increase the dietary intake of the amino acid phenylalenine in adults and to increase their body weight in children, they should not be

3. This is the list of official languages of the European Union

Włodarek et al., 2015). The products permitted include those that do not naturally contain phenylalanine. These include: honey, mineral water, vegetable oils, sugar, tea, fruit sugar.

4. Products authorised in limited quantities

Rocha, A. Restrictions should be placed on: potatoes, rice, ?? fruits and vegetables, ̇ butter and margarine, ̶ jam. Too much consumption can lead to an increase in the amount of amino acids in the blood (J.C. MacDonald 2016). These should be limited due to the content of phenylalanine.

5. Dietary guidelines for people with phenylketonuria

In addition to the above-mentioned symptoms, there are also special PKU stores and websites that offer such foods. Over time, this way of feeding becomes easier to use and the proper composition of existing meals is much faster. The dose should be adjusted accordingly, as is possible through consultation with your doctor and your dietitian. In addition, the symptoms of excess may include senescence, anemia and anorexia, which is caused by too low levels of amino acids in your blood. In order to better control your blood intake of this amino acid, it can be supplied in a special table.

6. For example, low-phenylalanine meals

2. Put the vegetables in a pot, soak them in water and cook them to softness (about 20 minutes).4. Pour the soup on a plate and add olive oil.

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Cook the pasta in braised water.2. Add spinach and soak it under cover for about 10 minutes.4. Place on a plate and add cut tomatoes. Preparation method1. Heat the olive oil on the pan and grease the cut onion cubes.3. After that, add the pre-cooked pasta and mix it thoroughly.5. Phenylalanine content: 93.3 mg Ingredients (per serving): PKU glass, olive oil teaspoon, onion plaster, spinax, leaves 2 bunches, cocktail tomatoes a bunch.

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Source

Jameson E., Remmington T., Dietary interventions for phenylketonuria, „Cochrane Database of Systematic Reviews” 2020, 7, 1–27.
Naz Al. H., Christodoulou J., Phenylketonuria: a review of current and future treatments, „Translational Pediatrics” 2015, 4(4), 304.
Program badań przesiewowych noworodków w Polsce na lata 2019–2022, Warszawa 2018.
Rocha J.C., MacDonald A., Dietary intervention in the management of phenylketonuria: current perspectives, „Pediatric health, medicine and therapeutics” 2016, 7, 155–163.
Włodarek D. et al., Dietoterapia, Warszawa 2015, 246–250.